Interleukin-33 overexpression reflects less aggressive tumour features in large-duct type cholangiocarcinomas

Histopathology. 2018 Aug;73(2):259-272. doi: 10.1111/his.13633. Epub 2018 May 30.

Abstract

Aims: The aim of the present study was to elucidate the clinicopathological significance of interleukin (IL)-6 and IL-33 expression in intrahepatic cholangiocarcinomas (iCCAs) and perihilar cholangiocarcinomas (pCCAs).

Methods and results: IL-6 and IL-33 mRNA expression levels were examined in iCCAs (n = 55) and pCCAs (n = 32) by the use of quantitative real-time polymerase chain reaction and a highly sensitive in-situ hybridisation protocol (RNAscope), and expression levels were correlated with clinicopathological features. According to a recently proposed classification scheme, iCCAs were separated into small-duct (n = 33) and large-duct (n = 22) types. IL-6 and IL-33 expression levels were higher in large-duct iCCAs and pCCAs than in small-duct iCCAs, and there was a positive correlation between the expression levels of these cytokines. Double in-situ hybridisation/immunostaining showed that IL-6 mRNA was expressed in actin-positive (myo)fibroblasts, whereas IL-33 mRNA was mainly produced by CD31-positive endothelial cells. With the average expression level as a cut-off point, cases were classified as IL-6high and IL-6low or IL-33high and IL-33low . In the combined cohort of large-duct iCCAs and pCCAs, IL-6high and IL-6low cholangiocarcinomas shared many features, whereas IL-33high cases had less aggressive characteristics than IL-33low cases, as shown by lower tumour marker concentrations, smaller tumour sizes, less common vascular invasion, lower pT stages, and higher lymphocyte/monocyte ratios in blood. KRAS mutations were slightly less common in IL-33high cases than in IL-33low cases (9% versus 29%; P = 0.061). The strong expression of IL-33 in tissue appeared to be an independent favourable prognostic factor.

Conclusions: IL-33high cholangiocarcinomas may represent a unique, less aggressive carcinogenetic process of the large bile ducts.

Keywords: IL-33; IL-6; cholangiocarcinoma; microenvironment; prognosis.

MeSH terms

  • Adult
  • Aged
  • Bile Duct Neoplasms / metabolism
  • Bile Duct Neoplasms / mortality
  • Bile Duct Neoplasms / pathology*
  • Bile Ducts, Intrahepatic / pathology
  • Biomarkers, Tumor / analysis*
  • Cholangiocarcinoma / metabolism
  • Cholangiocarcinoma / mortality
  • Cholangiocarcinoma / pathology*
  • Disease-Free Survival
  • Female
  • Humans
  • Interleukin-33 / analysis
  • Interleukin-33 / biosynthesis*
  • Interleukin-6 / analysis
  • Interleukin-6 / biosynthesis
  • Kaplan-Meier Estimate
  • Klatskin Tumor / metabolism
  • Klatskin Tumor / mortality
  • Klatskin Tumor / pathology*
  • Male
  • Middle Aged

Substances

  • Biomarkers, Tumor
  • IL33 protein, human
  • IL6 protein, human
  • Interleukin-33
  • Interleukin-6