Mesenteric tumour deposits arising from small-intestine neuroendocrine tumours are frequently associated with fibrosis and IgG4-expressing plasma cells

Histopathology. 2018 Nov;73(5):795-800. doi: 10.1111/his.13693. Epub 2018 Aug 13.

Abstract

Aims: Mesenteric tumour deposits frequently occur in small-intestine neuroendocrine tumours. In many instances, these mesenteric tumour deposits are surrounded by a dense fibrotic stroma and have associated lymphoplasmacytic inflammation. The aim of this study was to examine whether mesenteric tumour deposits in patients with small-intestine NETs neuroendocrine tumours show histological and immunophenotypic overlap with IgG4-related sclerosing mesenteritis.

Methods and results: Sixty-six mesenteric tumour deposits from 66 patients with small-intestine neuroendocrine tumours with blocks available for further studies were identified from our archives. Cases were assessed for clinicopathological features and the presence of IgG4-positive and IgG-positive plasma cells by immunohistochemistry. Ratios of IgG4-positive to IgG-positive plasma cells were calculated. Seventeen mesenteric tumour deposits (26%) showed >40 IgG4-positive plasma cells per high-power field, and the majority of cases (68%) showed at least some staining of IgG4-positive plasma cells. Mesenteric tumour deposits with >20 IgG4-positive plasma cells per high-power field tended to be larger (25.9 ± 13.0 mm versus 18.6 ± 15.8 mm; P = 0.07), and had more IgG-positive plasma cells (88 ± 24 versus 36 ± 37; P < 0.01) and a higher IgG4-positive/IgG-positive plasma cell ratio (0.66 ± 0.18 versus 0.17 ± 0.25; P < 0.01). All but one mesenteric tumour deposit with >20 IgG4-positve plasma cells had a ratio of >40%.

Conclusions: IgG4 expression is frequent in mesenteric tumour deposits from small-intestine neuroendocrine tumours. Undersampling of tumour on biopsies of mesenteric tumour deposits could potentially cause diagnostic confusion with IgG4-related sclerosing mesenteritis.

Keywords: IgG4; mesenteric tumour deposit; plasma cells; sclerosing mesenteritis; small-intestine neuroendocrine tumour.

MeSH terms

  • Adult
  • Aged
  • Aged, 80 and over
  • Diagnosis, Differential
  • Female
  • Fibrosis / pathology
  • Humans
  • Immunoglobulin G
  • Immunoglobulin G4-Related Disease / diagnosis
  • Intestinal Neoplasms / diagnosis
  • Intestinal Neoplasms / pathology*
  • Intestine, Small / pathology*
  • Male
  • Mesentery / pathology
  • Middle Aged
  • Neoplasm Metastasis / diagnosis
  • Neoplasm Metastasis / pathology*
  • Neuroendocrine Tumors / diagnosis
  • Neuroendocrine Tumors / pathology*
  • Panniculitis, Peritoneal / diagnosis
  • Plasma Cells / pathology
  • Young Adult

Substances

  • Immunoglobulin G