Clinical outcomes of adolescents and young adults with advanced solid tumours participating in phase I trials

Eur J Cancer. 2018 Sep:101:55-61. doi: 10.1016/j.ejca.2018.06.003. Epub 2018 Jul 17.

Abstract

Background: Adolescent and young adult (AYA) patients with advanced solid tumours are often considered for phase I clinical trials with novel agents. The outcome of AYAs in these trials have not been described before.

Aim: To study the outcome of AYA patients in phase I clinical trials.

Methods: Clinical trial data of AYAs (defined as aged 15-39 years at diagnosis) treated at the Drug Development Unit, Royal Marsden Hospital, between 2002 and 2016, were analysed.

Results: From a prospectively maintained database of 2631 patients treated in phase I trials, 219 AYA patients (8%) were identified. Major tumour types included gynaecological cancer (25%) and sarcoma (18%). Twenty-five (11%) had a known hereditary cancer syndrome (most commonly BRCA). Molecular characterisation of tumours (n = 45) identified mutations most commonly in TP53 (33%), PI3KCA (18%) and KRAS (9%). Therapeutic targets of trials included DNA damage repair (16%), phosphoinositide 3-kinase (PI3K) (16%) and angiogenesis (16%). Grade 3/4 toxicities were experienced in 26% of patients. Of the 214 evaluable patients, objective response rate was 12%, with clinical benefit rate at 6 months of 22%. Median overall survival (OS) was 7.5 months (95% confidence interval: 6.3-9.5), and 2-year OS was 11%. Of patients with responses, 36% were matched to phase I trials based on germline or somatic genetic aberrations.

Conclusion: We describe the outcome of the largest cohort of AYA patients treated in phase I trials. A subgroup of these patients demonstrates benefit, with several durable responses beyond 2 years. A sizeable proportion of AYA patients have cancer syndromes, significant family history or somatic molecular aberrancies which may influence novel therapeutic treatment options.

Keywords: Adolescents and young adults (AYAs); Advanced solid tumours; Cancer syndromes; Drug development; Phase I clinical trials.

Publication types

  • Clinical Trial, Phase I
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Adult
  • Antineoplastic Agents / adverse effects
  • Antineoplastic Agents / therapeutic use*
  • Cohort Studies
  • Fatigue / chemically induced
  • Humans
  • Kaplan-Meier Estimate
  • Mutation
  • Nausea / chemically induced
  • Neoplasms / classification
  • Neoplasms / drug therapy*
  • Neoplasms / genetics
  • Nuclear Proteins / genetics
  • Outcome Assessment, Health Care / methods
  • Outcome Assessment, Health Care / statistics & numerical data*
  • Proto-Oncogene Proteins p21(ras) / genetics
  • Transcription Factors / genetics
  • Tumor Suppressor Protein p53 / genetics
  • Vomiting / chemically induced
  • Young Adult

Substances

  • Antineoplastic Agents
  • KRAS protein, human
  • Nuclear Proteins
  • PI3KCA protein, human
  • TP53 protein, human
  • Transcription Factors
  • Tumor Suppressor Protein p53
  • Proto-Oncogene Proteins p21(ras)