Congenital anomalies of the pulmonary arteries: an imaging overview

Br J Radiol. 2019 Jan;92(1093):20180185. doi: 10.1259/bjr.20180185. Epub 2018 Aug 31.

Abstract

Congenital pulmonary artery anomalies represent a diverse group of abnormalities, ranging from asymptomatic incidental findings to causes of sudden cardiac death. While some may be recognized in childhood, others may be found incidentally in adulthood. We review the clinical and imaging findings in patients with congenital anomalies of the pulmonary arteries, including valvular and perivavular anomalies as well as abnormal narrowing, course and communications of the pulmonary arteries. We also discuss the role of various imaging modalities in the evaluation of these patients. It is vital to be aware of the key radiologic manifestations and associated haemodynamic consequences in these conditions in order to facilitate accurate diagnosis and prognostic stratification.

Publication types

  • Review

MeSH terms

  • Child, Preschool
  • Computed Tomography Angiography / methods
  • Female
  • Heart Defects, Congenital / diagnostic imaging*
  • Heart Defects, Congenital / epidemiology
  • Humans
  • Imaging, Three-Dimensional*
  • Incidence
  • Infant, Newborn
  • Magnetic Resonance Angiography / methods
  • Male
  • Middle Aged
  • Prognosis
  • Pulmonary Artery / abnormalities*
  • Pulmonary Artery / diagnostic imaging*
  • Pulmonary Valve Stenosis / congenital
  • Pulmonary Valve Stenosis / diagnostic imaging*
  • Pulmonary Valve Stenosis / epidemiology
  • Risk Assessment