Management of a rare presentation of Kindler disease with digital constriction bands-Case report

Pediatr Dermatol. 2018 Nov;35(6):864-865. doi: 10.1111/pde.13674. Epub 2018 Sep 6.

Abstract

Kindler disease is a type of epidermolysis bullosa associated with acral blistering, diffuse cutaneous atrophy, poikiloderma, mucosal stenosis, and photosensitivity. This is the first case report in the literature to describe constriction bands associated with Kindler disease causing ischemia of the fingertips requiring urgent release and full-thickness skin grafts. Dermatologists reviewing such patients need to be aware of this condition and refer to a children's hand surgeon early to avoid leaving patients with prolonged periods of pain.

Keywords: Kindler disease; constriction bands; digital constriction; epidermolysis bullosa.

Publication types

  • Case Reports

MeSH terms

  • Adolescent
  • Blister / complications*
  • Blister / surgery
  • Constriction, Pathologic
  • Epidermolysis Bullosa / complications*
  • Epidermolysis Bullosa / surgery
  • Female
  • Fingers / pathology*
  • Fingers / surgery
  • Humans
  • Periodontal Diseases / complications*
  • Periodontal Diseases / surgery
  • Photosensitivity Disorders / complications*
  • Photosensitivity Disorders / surgery
  • Skin / pathology*

Supplementary concepts

  • Poikiloderma of Kindler