Population-based trends in the prenatal diagnosis of sex chromosome aneuploidy before and after non-invasive prenatal testing

Prenat Diagn. 2018 Dec;38(13):1062-1068. doi: 10.1002/pd.5363. Epub 2018 Oct 30.

Abstract

Objective: To assess the impact of non-invasive prenatal testing (NIPT) on trends in the prenatal diagnosis of sex chromosome aneuploidy (SCA) in a population with >73,000 annual births.

Method: Retrospective population-based cohort study from 1986-2016 of all women undergoing prenatal diagnosis before 25 weeks gestation in the Australian state of Victoria. Statistical significance was tested using the chi-square test for trend or proportions.

Results: There were 2,043,345 births and 842 SCA diagnoses from 1986-2016. The percentage of prenatal diagnostic tests leading to a SCA diagnosis increased significantly from 0.95% in 2010 to 2.93% in 2016 (p < 0.001) but due to a concurrent decline in testing, the annual prenatal diagnosis rate of SCA remained stable at 4.4/10,000 births. Among confirmed fetal SCAs the most common indication for testing in 1986 was advanced maternal age (63%); in 2016 it was high risk NIPT (49%).

Conclusion: SCAs now make up an increasing proportion of prenatal diagnostic results but due to the overall decline in diagnostic testing, the prenatal prevalence as a percentage of births remained steady. The ascertainment of fetal SCA has evolved from an incidental finding after testing for increased risk of trisomy 21, to a diagnosis obtained after suspected SCA on NIPT.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Amniocentesis
  • Aneuploidy*
  • Chorionic Villi Sampling
  • Chromosomes, Human, X
  • Female
  • Humans
  • Klinefelter Syndrome / diagnosis
  • Klinefelter Syndrome / epidemiology*
  • Mosaicism / statistics & numerical data
  • Pregnancy
  • Prenatal Diagnosis
  • Retrospective Studies
  • Sex Chromosome Aberrations / statistics & numerical data
  • Sex Chromosome Disorders of Sex Development / diagnosis
  • Sex Chromosome Disorders of Sex Development / epidemiology*
  • Trisomy / diagnosis
  • Turner Syndrome / diagnosis
  • Turner Syndrome / epidemiology*
  • Ultrasonography, Prenatal
  • Victoria / epidemiology
  • XYY Karyotype / diagnosis
  • XYY Karyotype / epidemiology*

Supplementary concepts

  • Triple X syndrome