Delays in Diagnosis of Pediatric Histologically Confirmed Sellar Germ Cell Tumors in China: A Retrospective Risk Factor Analysis

World Neurosurg. 2019 Feb:122:e472-e479. doi: 10.1016/j.wneu.2018.10.082. Epub 2018 Oct 24.

Abstract

Background: Sellar germ cell tumors (GCTs) occur more frequently in childhood. Some will present as malignancy with infiltration and metastasis. However, the association between the timeliness of diagnosis and outcome has been controversial. We investigated the clinical risk factors associated with a diagnostic delay in patients with sellar GCTs in China.

Methods: The data from 53 patients aged <18 years with histologically confirmed sellar GCTs at Peking Union Medical College Hospital treated from January 2008 to December 2016 were reviewed retrospectively.

Results: The median interval between symptom onset and diagnosis was 25 months. Of the 53 patients, 44 (83%) had a delayed diagnosis. Most patients (86%) with a delayed diagnosis presented with polyuria or polydipsia. Of the 53 patients, 48 (91%) exhibited changes in the pituitary stalk. Patients with a germinoma (odds ratio, 4.1; 95% confidence interval, 2.4-6.9) and slow growth (odds ratio, 5.3; 95% confidence interval, 1.2-24.5) were more likely to have a delayed diagnosis. The overwhelming majority of patients with a delayed diagnosis (96%) had been seen by >1 doctor. No statistically significant differences were found in the mean survival time (P = 0.21) or mean progression-free survival time (P = 0.36) between patients with and without delay in diagnosis, respectively.

Conclusions: A significant proportion of patients with sellar GCTs will experience a delay in the time to diagnosis. Although a delay in diagnosis did not reduce the survival time or progression-free survival time for patients with sellar GCTs, it might increase the risk of short stature. Thus, a detailed medical history and an immediate radiological examination are important for the early diagnosis of sellar GCTs in childhood.

Keywords: Delayed diagnosis; Histological confirmation; Pediatric sellar germ cell tumors; Risk factors.

MeSH terms

  • Adolescent
  • Child
  • Child, Preschool
  • China / epidemiology
  • Delayed Diagnosis / mortality
  • Delayed Diagnosis / trends*
  • Female
  • Follow-Up Studies
  • Humans
  • Infant
  • Male
  • Neoplasms, Germ Cell and Embryonal / diagnostic imaging*
  • Neoplasms, Germ Cell and Embryonal / mortality
  • Neoplasms, Germ Cell and Embryonal / surgery
  • Pituitary Neoplasms / diagnostic imaging*
  • Pituitary Neoplasms / mortality
  • Pituitary Neoplasms / surgery
  • Retrospective Studies
  • Risk Factors
  • Sella Turcica / diagnostic imaging*
  • Sella Turcica / surgery