Gboxin is an oxidative phosphorylation inhibitor that targets glioblastoma

Nature. 2019 Mar;567(7748):341-346. doi: 10.1038/s41586-019-0993-x. Epub 2019 Mar 6.

Abstract

Cancer-specific inhibitors that reflect the unique metabolic needs of cancer cells are rare. Here we describe Gboxin, a small molecule that specifically inhibits the growth of primary mouse and human glioblastoma cells but not that of mouse embryonic fibroblasts or neonatal astrocytes. Gboxin rapidly and irreversibly compromises oxygen consumption in glioblastoma cells. Gboxin relies on its positive charge to associate with mitochondrial oxidative phosphorylation complexes in a manner that is dependent on the proton gradient of the inner mitochondrial membrane, and it inhibits the activity of F0F1 ATP synthase. Gboxin-resistant cells require a functional mitochondrial permeability transition pore that regulates pH and thus impedes the accumulation of Gboxin in the mitochondrial matrix. Administration of a metabolically stable Gboxin analogue inhibits glioblastoma allografts and patient-derived xenografts. Gboxin toxicity extends to established human cancer cell lines of diverse organ origin, and shows that the increased proton gradient and pH in cancer cell mitochondria is a mode of action that can be targeted in the development of antitumour reagents.

MeSH terms

  • Allografts
  • Animals
  • Astrocytes / cytology
  • Astrocytes / drug effects
  • Cell Line, Tumor
  • Fibroblasts / cytology
  • Fibroblasts / drug effects
  • Glioblastoma / drug therapy*
  • Glioblastoma / metabolism*
  • Humans
  • Hydrogen-Ion Concentration
  • Mice
  • Mitochondrial Membrane Transport Proteins / metabolism
  • Mitochondrial Membranes / drug effects
  • Mitochondrial Membranes / enzymology
  • Mitochondrial Membranes / metabolism
  • Mitochondrial Permeability Transition Pore
  • Neoplasm Transplantation
  • Organ Specificity
  • Oxidative Phosphorylation / drug effects*
  • Proton-Motive Force / drug effects
  • Proton-Translocating ATPases / antagonists & inhibitors
  • Proton-Translocating ATPases / metabolism
  • Xenograft Model Antitumor Assays

Substances

  • Mitochondrial Membrane Transport Proteins
  • Mitochondrial Permeability Transition Pore
  • Proton-Translocating ATPases