Investigation into the α-Gal Syndrome: Characteristics of 261 Children and Adults Reporting Red Meat Allergy

J Allergy Clin Immunol Pract. 2019 Sep-Oct;7(7):2348-2358.e4. doi: 10.1016/j.jaip.2019.03.031. Epub 2019 Mar 30.

Abstract

Background: Red meat allergy has historically been understood as a rare disease of atopic children, but the discovery of the "α-Gal syndrome," which relates to IgE to the oligosaccharide galactose-α-1,3-galactose (α-Gal), has challenged that notion.

Objective: To describe the clinical and immunologic characteristics of a large group of subjects with self-reported allergy to mammalian meat.

Methods: This was an observational study of 261 children and adults (range, 5-82 years) who presented for evaluation for allergic reactions to mammalian meat. Results were based on serum assays and a detailed questionnaire.

Results: α-Gal specific IgE ≥ 0.35 IU/mL was detected in 245 subjects and symptom onset occurred ≥2 hours after eating mammalian meat in 211 (81%). Component testing supported a diagnosis of α-Gal syndrome in 95%, pork-cat syndrome in 1.9%, and primary beef allergy in 1.1%. Urticaria was reported by 93%, anaphylaxis by 60%, and gastrointestinal symptoms by 64%. Levels of IgE and IgG specific to α-Gal were similar in subjects who reported early- or delayed-onset symptoms, and in those with and without anaphylaxis. Levels of α-Gal specific IgE and severity of reactions were similar among those with and without traditional atopy, and among children (n = 35) and adults (n = 226). Blood group B trended toward being under-represented among α-Gal-sensitized subjects; however, α-Gal specific IgE titers were high in symptomatic cases with B-antigen.

Conclusions: The α-Gal syndrome is a regionally common form of food allergy that has a characteristic but not universal delay in symptom onset, includes gastrointestinal symptoms, can develop at any time in life, and is equally common in otherwise nonatopic individuals.

Keywords: Alpha-gal; Anaphylaxis; Food allergy; Galactose-α-1,3-galactose; Red meat.

Publication types

  • Observational Study
  • Research Support, N.I.H., Extramural

MeSH terms

  • Adolescent
  • Adult
  • Aged
  • Aged, 80 and over
  • Allergens / adverse effects*
  • Anaphylaxis / blood
  • Anaphylaxis / etiology
  • Child
  • Child, Preschool
  • Female
  • Food Hypersensitivity* / blood
  • Food Hypersensitivity* / complications
  • Humans
  • Immunoglobulin E / blood
  • Immunoglobulin G / blood
  • Male
  • Meat / adverse effects*
  • Middle Aged
  • Syndrome
  • Tick-Borne Diseases* / blood
  • Tick-Borne Diseases* / complications
  • Urticaria / blood
  • Urticaria / etiology
  • Young Adult

Substances

  • Allergens
  • Immunoglobulin G
  • Immunoglobulin E

Supplementary concepts

  • red meat allergy