PD-L1 expressing granulomatous reaction as an on-target mechanism of steroid-refractory immune hepatotoxicity

Immunotherapy. 2019 May;11(7):585-590. doi: 10.2217/imt-2018-0187.

Abstract

Immune-related hepatitis is an important toxicity from immune-checkpoint inhibitor therapy, affecting up to 20% of patients on dual cytotoxic T-lymphocyte antigen 4/programmed cell death 1 (CTLA-4/PD-1) inhibitors. The mechanisms underlying this type of drug-induced liver injury are poorly understood. We report the case of a patient with immune-checkpoint inhibitor-related hepatitis where the presence of a diffuse granulomatous, PD-L1-positive infiltrate on liver biopsy correlated with poor response to corticosteroids. Our findings suggest a potential role for activation of the PD-1 pathway within the histiocitic infiltrate as a mechanism of toxicity. Further studies should address the role of macrophages in this patient group characterized by steroid-refractoriness.

Keywords: DILI; hepatitis; hepatotoxicity; immune checkpoint inhibitors; toxicity.

Publication types

  • Case Reports

MeSH terms

  • Adrenal Cortex Hormones / therapeutic use
  • Antineoplastic Combined Chemotherapy Protocols / adverse effects
  • Antineoplastic Combined Chemotherapy Protocols / therapeutic use*
  • B7-H1 Antigen / genetics
  • B7-H1 Antigen / metabolism
  • Biopsy
  • CTLA-4 Antigen / antagonists & inhibitors
  • Drug Resistance
  • Drug-Related Side Effects and Adverse Reactions / diagnosis*
  • Granuloma / diagnosis*
  • Granuloma / etiology
  • Hepatitis / diagnosis*
  • Hepatitis / etiology
  • Humans
  • Immunotherapy / adverse effects
  • Immunotherapy / methods*
  • Ipilimumab / adverse effects
  • Ipilimumab / therapeutic use*
  • Liver / metabolism*
  • Liver / pathology
  • Macrophages / immunology
  • Male
  • Melanoma / drug therapy*
  • Middle Aged
  • Neoplasms, Unknown Primary / drug therapy*
  • Nivolumab / adverse effects
  • Nivolumab / therapeutic use*
  • Programmed Cell Death 1 Receptor / antagonists & inhibitors

Substances

  • Adrenal Cortex Hormones
  • B7-H1 Antigen
  • CD274 protein, human
  • CTLA-4 Antigen
  • CTLA4 protein, human
  • Ipilimumab
  • PDCD1 protein, human
  • Programmed Cell Death 1 Receptor
  • Nivolumab