Effectiveness of ivacaftor in cystic fibrosis: Improvement of liver cirrhosis, nutritional status and respiratory function

Med Clin (Barc). 2020 Jul 24;155(2):82-83. doi: 10.1016/j.medcli.2019.02.011. Epub 2019 Apr 11.

[Article in English, Spanish]

Authors

Carlos Martín de Vicente¹, Ruth García Romero²

Affiliations

¹ Unidad de Neumología Pediátrica y Fibrosis Quística, Hospital Infantil Miguel Servet, Zaragoza, España. Electronic address: [email protected].
² Unidad de Gastroenterología Pediátrica y Fibrosis Quística, Hospital Infantil Miguel Servet, Zaragoza, España.

PMID: 30982531
DOI: 10.1016/j.medcli.2019.02.011

No abstract available

Publication types

Case Reports
Letter

MeSH terms

Aminophenols / therapeutic use
Cystic Fibrosis* / complications
Cystic Fibrosis* / drug therapy
Forced Expiratory Volume
Humans
Liver Cirrhosis / complications
Liver Cirrhosis / drug therapy
Mutation
Nutritional Status
Quinolones

Substances

Aminophenols
Quinolones
ivacaftor