Splenorenal fusion is an extremely rare benign entity. This abnormality is presented in a case of a 29-year-old-male patient. We discuss the distinction between this condition and renal splenosis and their embryology. The course of this condition and modalities of investigation including radiological imaging, management, and pitfalls are reviewed.
Keywords: Accessory spleen; ectopic spleen; splenic heterotopia; splenorenal fusion; splenosis.