Clinical outcomes after the endovascular treatments of pulmonary vein stenosis in patients with congenital heart disease

Cardiol Young. 2019 Aug;29(8):1057-1065. doi: 10.1017/S1047951119001495. Epub 2019 Jul 9.

Abstract

Background: Pulmonary vein stenosis (PVS) is a condition with challenging treatment and leads to severe cardiac failure and pulmonary hypertension. Despite aggressive surgical or catheter-based intervention, the prognosis of PVS is unsatisfactory. This study aimed to assess the prognosis and to establish appropriate treatment strategies.

Methods: We retrospectively reviewed endovascular treatments for PVS (2001-2017) from the clinical database at the Okayama University Hospital.

Results: A total of 24 patients underwent PVS associated with total anomalous pulmonary venous connection and 7 patients underwent isolated congenital PVS. In total, 53 stenotic pulmonary veins were subjected to endovascular treatments; 40 of them were stented by hybrid (29) and percutaneous procedures (11) (bare-metal stent, n = 34; drug-eluting stent, n = 9). Stent size of hybrid stenting was larger than percutaneous stenting. Median follow-up duration from the onset of PVS was 24 months (4-134 months). Survival rate was 71 and 49% at 1 and 5 years, respectively. There was no statistically significant difference between stent placement and survival; however, patients who underwent bare-metal stent implantation had statistically better survival than those who underwent drug-eluting stent implantation or balloon angioplasty. Early onset of stenosis, timing of stenting, and small vessel diameter of pulmonary vein before stenting were considered as risk factors for in-stent restenosis. Freedom from re-intervention was 50 and 26% at 1 and 2 years.

Conclusions: To improve survival and stent patency, implantation of large stent is important. However, re-intervention after stenting is also significant to obtain good outcome.

Keywords: Pulmonary vein stenosis; balloon angioplasty; hybrid stent implantation; isolated congenital pulmonary vein stenosis; re-intervention for stent; total anomalous of pulmonary venous connection.

MeSH terms

  • Angioplasty, Balloon / methods
  • Blood Vessel Prosthesis Implantation*
  • Child, Preschool
  • Drug-Eluting Stents
  • Female
  • Humans
  • Infant
  • Male
  • Retrospective Studies
  • Risk Factors
  • Scimitar Syndrome / mortality
  • Scimitar Syndrome / pathology
  • Scimitar Syndrome / surgery*
  • Stenosis, Pulmonary Vein / congenital*
  • Stenosis, Pulmonary Vein / mortality
  • Stenosis, Pulmonary Vein / surgery*
  • Survival Analysis
  • Treatment Outcome