Consensus criteria for diagnosis, staging, and treatment response assessment of T-cell prolymphocytic leukemia

Blood. 2019 Oct 3;134(14):1132-1143. doi: 10.1182/blood.2019000402. Epub 2019 Jul 10.

Abstract

T-cell prolymphocytic leukemia (T-PLL) is a rare, mature T-cell neoplasm with a heterogeneous clinical course. With the advent of novel treatment options that will potentially change the management of patients with T-PLL, it has become necessary to produce consensus guidelines for the design and conduct of clinical trials. The T-PLL International Study group (TPLL-ISG) set out to define standardized criteria for diagnosis, treatment indication, and evaluation of response. These criteria will facilitate comparison of results from clinical trials in T-PLL, and will thus support clinical decision making, as well as the approval of new therapeutics by healthcare authorities.

Publication types

  • Review

MeSH terms

  • Bone Marrow / pathology
  • Disease Management
  • Gene Expression Regulation, Leukemic
  • Humans
  • Immunophenotyping
  • Leukemia, Prolymphocytic, T-Cell / diagnosis*
  • Leukemia, Prolymphocytic, T-Cell / genetics
  • Leukemia, Prolymphocytic, T-Cell / pathology
  • Leukemia, Prolymphocytic, T-Cell / therapy*
  • Mutation
  • Neoplasm Staging
  • T-Lymphocytes / pathology