CABLES1 Deficiency Impairs Quiescence and Stress Responses of Hematopoietic Stem Cells in Intrinsic and Extrinsic Manners

Stem Cell Reports. 2019 Aug 13;13(2):274-290. doi: 10.1016/j.stemcr.2019.06.002. Epub 2019 Jul 18.

Abstract

Bone marrow (BM) niche cells help to keep adult hematopoietic stem cells (HSCs) in a quiescent state via secreted factors and induction of cell-cycle inhibitors. Here, we demonstrate that the adapter protein CABLES1 is a key regulator of long-term hematopoietic homeostasis during stress and aging. Young mice lacking Cables1 displayed hyperproliferation of hematopoietic progenitor cells. This defect was cell intrinsic, since it was reproduced in BM transplantation assays using wild-type animals as recipients. Overexpression and short hairpin RNA-mediated depletion of CABLES1 protein resulted in p21Cip/waf up- and downregulation, respectively. Aged mice lacking Cables1 displayed abnormalities in peripheral blood cell counts accompanied by a significant reduction in HSC compartment, concomitant with an increased mobilization of progenitor cells. In addition, Cables1-/- mice displayed increased sensitivity to the chemotherapeutic agent 5-fluorouracil due to an abnormal microenvironment. Altogether, our findings uncover a key role for CABLES1 in HSC homeostasis and stress hematopoiesis.

Keywords: CABLES1; cell cycle; hematopoietic niches; hematopoietic stem cell homeostasis; mesenchymal stromal cells; p21.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Aging
  • Animals
  • Antigens, CD34 / metabolism
  • Bone Marrow Cells / cytology
  • Cell Cycle Checkpoints / drug effects
  • Cell Proliferation
  • Cyclin-Dependent Kinase Inhibitor p21 / metabolism
  • Cyclins / antagonists & inhibitors
  • Cyclins / genetics*
  • Cyclins / metabolism
  • Fluorouracil / pharmacology
  • Hematopoiesis / drug effects
  • Hematopoietic Stem Cell Transplantation
  • Hematopoietic Stem Cells / cytology*
  • Hematopoietic Stem Cells / metabolism
  • Humans
  • Lipopolysaccharides / pharmacology
  • Mice
  • Mice, Inbred C57BL
  • Mice, Knockout
  • RNA Interference
  • RNA, Small Interfering / metabolism

Substances

  • Antigens, CD34
  • Cables1 protein, mouse
  • Cyclin-Dependent Kinase Inhibitor p21
  • Cyclins
  • Lipopolysaccharides
  • RNA, Small Interfering
  • Fluorouracil