The E3 ubiquitin ligase SPOP controls resolution of systemic inflammation by triggering MYD88 degradation

Nat Immunol. 2019 Sep;20(9):1196-1207. doi: 10.1038/s41590-019-0454-6. Epub 2019 Aug 12.

Abstract

The response to systemic infection and injury requires the rapid adaptation of hematopoietic stem cells (HSCs), which proliferate and divert their differentiation toward the myeloid lineage. Significant interest has emerged in understanding the signals that trigger the emergency hematopoietic program. However, the mechanisms that halt this response of HSCs, which is critical to restore homeostasis, remain unknown. Here we reveal that the E3 ubiquitin ligase Speckle-type BTB-POZ protein (SPOP) restrains the inflammatory activation of HSCs. In the absence of Spop, systemic inflammation proceeded in an unresolved manner, and the sustained response in the HSCs resulted in a lethal phenotype reminiscent of hyper-inflammatory syndrome or sepsis. Our proteomic studies decipher that SPOP restricted inflammation by ubiquitinating the innate signal transducer myeloid differentiation primary response protein 88 (MYD88). These findings unearth an HSC-intrinsic post-translational mechanism that is essential for reestablishing homeostasis after emergency hematopoiesis.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Cell Line
  • Female
  • HEK293 Cells
  • Hematopoiesis / immunology
  • Humans
  • Inflammation / immunology*
  • Leukocytosis / immunology*
  • Male
  • Mice
  • Myeloid Differentiation Factor 88 / metabolism*
  • Neutrophils / cytology
  • Neutrophils / immunology*
  • Nuclear Proteins / metabolism*
  • Repressor Proteins / metabolism*
  • Ubiquitin-Protein Ligase Complexes
  • Ubiquitin-Protein Ligases / metabolism

Substances

  • Myd88 protein, mouse
  • Myeloid Differentiation Factor 88
  • Nuclear Proteins
  • Repressor Proteins
  • Spop protein, mouse
  • Ubiquitin-Protein Ligase Complexes
  • Ubiquitin-Protein Ligases