Left Ventricle to Right Atrial Shunt Associated With Ventricular-Atrial Malalignment, Double Outlet Right Atrium, and Subaortic Membrane

Timothy Guenther; Luis Godoy; Sarah Chen; Jay Yeh; Gary Raff

doi:10.1053/j.semtcvs.2019.09.004

Left Ventricle to Right Atrial Shunt Associated With Ventricular-Atrial Malalignment, Double Outlet Right Atrium, and Subaortic Membrane

Semin Thorac Cardiovasc Surg. 2020 Spring;32(1):140-142. doi: 10.1053/j.semtcvs.2019.09.004. Epub 2019 Sep 11.

Authors

Timothy Guenther¹, Luis Godoy², Sarah Chen², Jay Yeh³, Gary Raff²

Affiliations

¹ Department of Surgery, University of California Davis, Sacramento, California. Electronic address: [email protected].
² Department of Surgery, University of California Davis, Sacramento, California.
³ Department of Pediatrics, University of California Davis, Sacramento, California.

PMID: 31520731
DOI: 10.1053/j.semtcvs.2019.09.004

Abstract

We describe an asymptomatic 7-year-old boy who was taken to the operating room for repair of a subaortic membrane and possible Gerbode's defect. He was found to have a double outlet right atrium associated with an accessory atrioventricular valve in addition to a small atrial septal defect and subaortic membrane. Regurgitant flow through this accessory valve led to the left ventricle to right atrial shunt that was seen on preoperative ECHO. The atrial septal defect was repaired and a baffle was used to isolate blood flow across the accessory valve from the left atrium to the left ventricle. The patient was discharged on postoperative day 4 and has been doing well 2 years postoperatively.

Keywords: Double outlet right atrium; Left ventricle to right atrium shunt.

Publication types

Case Reports
Video-Audio Media

MeSH terms

Abnormalities, Multiple*
Asymptomatic Diseases
Cardiac Surgical Procedures*
Child
Discrete Subaortic Stenosis / diagnostic imaging
Discrete Subaortic Stenosis / physiopathology
Discrete Subaortic Stenosis / surgery*
Heart Atria / abnormalities
Heart Atria / diagnostic imaging
Heart Atria / physiopathology
Heart Atria / surgery*
Heart Defects, Congenital / diagnostic imaging
Heart Defects, Congenital / physiopathology
Heart Defects, Congenital / surgery*
Heart Septal Defects, Atrial / diagnostic imaging
Heart Septal Defects, Atrial / physiopathology
Heart Septal Defects, Atrial / surgery*
Heart Valves / abnormalities
Heart Valves / diagnostic imaging
Heart Valves / physiopathology
Heart Valves / surgery*
Hemodynamics*
Humans
Male
Recovery of Function
Treatment Outcome

Supplementary concepts

Subaortic Stenosis, Membranous