Abstract
The investigational drugs E7820, indisulam and tasisulam (aryl-sulfonamides) promote the degradation of the splicing factor RBM39 in a proteasome-dependent mechanism. While the activity critically depends on the cullin RING ligase substrate receptor DCAF15, the molecular details remain elusive. Here we present the cryo-EM structure of the DDB1-DCAF15-DDA1 core ligase complex bound to RBM39 and E7820 at a resolution of 4.4 Å, together with crystal structures of engineered subcomplexes. We show that DCAF15 adopts a new fold stabilized by DDA1, and that extensive protein-protein contacts between the ligase and substrate mitigate low affinity interactions between aryl-sulfonamides and DCAF15. Our data demonstrate how aryl-sulfonamides neo-functionalize a shallow, non-conserved pocket on DCAF15 to selectively bind and degrade RBM39 and the closely related splicing factor RBM23 without the requirement for a high-affinity ligand, which has broad implications for the de novo discovery of molecular glue degraders.
Publication types
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Research Support, N.I.H., Extramural
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Research Support, Non-U.S. Gov't
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Research Support, U.S. Gov't, Non-P.H.S.
MeSH terms
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Amino Acid Motifs
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Animals
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Benzamides / chemistry
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Benzamides / pharmacology
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Cryoelectron Microscopy
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Fluorescence Resonance Energy Transfer
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Humans
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Indoles / chemistry*
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Indoles / pharmacology
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Intracellular Signaling Peptides and Proteins / chemistry*
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Intracellular Signaling Peptides and Proteins / metabolism
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Kinetics
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Protein Binding
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Protein Domains
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Protein Interaction Mapping
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Protein Structure, Secondary
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Proteolysis / drug effects*
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RNA Recognition Motif Proteins / chemistry*
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RNA Recognition Motif Proteins / metabolism
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RNA-Binding Proteins
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Spodoptera
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Sulfonamides / chemistry*
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Sulfonamides / pharmacology
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Ubiquitin-Protein Ligases / chemistry
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Xenopus
Substances
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Benzamides
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DCAF15 protein, human
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HCC1 autoantigen
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IL17RB protein, human
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Indoles
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Intracellular Signaling Peptides and Proteins
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N-((5-bromo-2-thienyl)sulfonyl)-2,4-dichlorobenzamide
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N-(3-chloro-7-indolyl)-1,4-benzenedisulphonamide
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RBM23 protein, human
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RNA Recognition Motif Proteins
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RNA-Binding Proteins
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Sulfonamides
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N-(3-cyano-4-methyl-1H-indol-7-yl)-3-cyanobenzene-sulfonamide
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Ubiquitin-Protein Ligases