Pediatric Extraskeletal Ewing Sarcoma Originating in the Heart: A Case Report and Review of the Literature

Isabella Buffoni; Halkawt Nuri; Giuseppe Pome'; Angela R Sementa; Nicola Stagnaro; Salvina Barra; Carla Manzitti; Alberto Garaventa

doi:10.1097/MPH.0000000000001622

Pediatric Extraskeletal Ewing Sarcoma Originating in the Heart: A Case Report and Review of the Literature

J Pediatr Hematol Oncol. 2021 May 1;43(4):147-151. doi: 10.1097/MPH.0000000000001622.

Authors

Isabella Buffoni¹, Halkawt Nuri², Giuseppe Pome'², Angela R Sementa³, Nicola Stagnaro⁴, Salvina Barra⁵, Carla Manzitti¹, Alberto Garaventa¹

Affiliations

¹ Department of Haematology-Oncology.
² Cardiac Surgery Unit.
³ Pathology Unit.
⁴ Radiology Unit, Giannina Gaslini Institute.
⁵ Radiotherapy Unit, San Martino Polyclinic Hospital, Genoa, Italy.

PMID: 31688622
DOI: 10.1097/MPH.0000000000001622

Abstract

Extraosseous Ewing sarcoma of primary cardiac origin is an extremely rare variety among pediatric cardiac neoplasms. We report a case of extraosseous Ewing sarcoma of primary cardiac origin in a 9-year-old girl, treated with debulking surgery, adjuvant chemotherapy, and radiotherapy.

Publication types

Case Reports
Review

MeSH terms

Antineoplastic Combined Chemotherapy Protocols / therapeutic use
Chemotherapy, Adjuvant
Child
Female
Heart Neoplasms / drug therapy
Heart Neoplasms / pathology*
Heart Neoplasms / radiotherapy
Heart Neoplasms / surgery
Humans
Myocardium / pathology*
Sarcoma, Ewing / drug therapy
Sarcoma, Ewing / pathology*
Sarcoma, Ewing / radiotherapy
Sarcoma, Ewing / surgery