Prenatal ultrasound diagnosis of fetal isolated right ventricular noncompaction with pulmonary artery sling: A rare case report

Echocardiography. 2019 Nov;36(11):2118-2121. doi: 10.1111/echo.14528. Epub 2019 Nov 6.

Abstract

Noncompaction of the ventricular myocardium (NVM), also known as spongy myocardium, is a rare type of cardiomyopathy that has a serious impact on fetuses, children, and adults. NVM mainly affects the left ventricle, as isolated right ventricular noncompaction (IRVNC) is rare. Pulmonary artery sling (PAS) is a rare condition in which the left pulmonary artery anomalously originates from a normal positioned right pulmonary artery, and only a few studies have reported PAS in fetuses. Fetal IRVNC complicated with PAS has not been reported yet. Here, we report a case of IRVNC complicated with PAS that was diagnosed prenatally at 30 weeks gestation and confirmed by postpartum anatomy and pathology.

Keywords: fetus; isolated right ventricular noncompaction; pulmonary artery sling.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Echocardiography, Doppler, Color / methods*
  • Fatal Outcome
  • Female
  • Fetal Heart / diagnostic imaging*
  • Gestational Age
  • Heart Ventricles / abnormalities*
  • Heart Ventricles / diagnostic imaging
  • Heart Ventricles / embryology
  • Humans
  • Infant, Newborn
  • Isolated Noncompaction of the Ventricular Myocardium / diagnosis*
  • Isolated Noncompaction of the Ventricular Myocardium / embryology
  • Pregnancy
  • Pulmonary Artery / abnormalities*
  • Pulmonary Artery / diagnostic imaging
  • Pulmonary Artery / embryology
  • Rare Diseases
  • Ultrasonography, Prenatal / methods*
  • Vascular Malformations / diagnosis*
  • Vascular Malformations / embryology