The frequency of longitudinally extensive transverse myelitis in MS: A population-based study

Mult Scler Relat Disord. 2020 Jan:37:101487. doi: 10.1016/j.msard.2019.101487. Epub 2019 Oct 31.

Abstract

Background: Determining the frequency of longitudinally-extensive transverse myelitis (LETM: T2-lesion ≥3 vertebral segments) in multiple sclerosis (MS) is essential to assess its utility in differentiating from aquaporin-4-IgG (AQP4-IgG) positive neuromyelitis optica spectrum disorder (NMOSD) and myelin-oligodendrocyte-glycoprotein-IgG (MOG-IgG) myelitis. We sought to determine the frequency of LETM in MS during a myelitis attack.

Methods: We identified Olmsted County (MN, USA) residents on 12/31/2011 with inflammatory demyelinating disease. Inclusion criteria were: 1) Clinical myelitis episode accompanied by a new spinal magnetic resonance imaging (MRI) lesion (≤6 weeks from onset); 2) MS diagnosis by 2010 McDonald criteria; 3) Seronegative for AQP4-IgG and MOG-IgG. MRI characteristics were determined.

Results: Sixty-seven patients (median age at myelitis: 41 years [range, 16-65]; 76% females) with 92 myelitis attacks accompanied by a new MRI spinal cord lesion were identified. The frequency of LETM was 0%. The median T2-hyperintense lesion length in vertebral segments was 1.0 (range, 0.5-2.5) and 82/92 (89%) were peripheral in location on axial sequences; 58% had associated gadolinium enhancement. Two patients (2% of attacks) had multiple short lesions resembling LETM on sagittal images but axial sequences confirmed multiple non-contiguous short lesions.

Conclusion: LETM is rare in adult MS myelitis and its presence should prompt evaluation for AQP4-IgG, MOG-IgG or other etiologies. Careful scrutiny of axial images is important as coalescence of multiple short lesions may lead to the artifactual appearance of an LETM.

Keywords: Aquaporin-4; Longitudinally extensive spinal cord lesion; Longitudinally extensive transverse myelitis; Multiple sclerosis; Myelin oligodendrocyte glycoprotein; Myelitis.

MeSH terms

  • Adolescent
  • Adult
  • Aged
  • Aquaporin 4 / immunology
  • Biological Specimen Banks
  • Female
  • Humans
  • Magnetic Resonance Imaging
  • Male
  • Middle Aged
  • Minnesota / epidemiology
  • Multiple Sclerosis* / diagnostic imaging
  • Multiple Sclerosis* / epidemiology
  • Multiple Sclerosis* / immunology
  • Multiple Sclerosis* / pathology
  • Myelin-Oligodendrocyte Glycoprotein / immunology
  • Myelitis, Transverse* / diagnostic imaging
  • Myelitis, Transverse* / epidemiology
  • Myelitis, Transverse* / immunology
  • Myelitis, Transverse* / pathology
  • Young Adult

Substances

  • AQP4 protein, human
  • Aquaporin 4
  • MOG protein, human
  • Myelin-Oligodendrocyte Glycoprotein