Differential Modes of Orphan Subunit Recognition for the WRB/CAML Complex

Cell Rep. 2020 Mar 17;30(11):3691-3698.e5. doi: 10.1016/j.celrep.2020.02.084.

Abstract

A large proportion of membrane proteins must be assembled into oligomeric complexes for function. How this process occurs is poorly understood, but it is clear that complex assembly must be tightly regulated to avoid accumulation of orphan subunits with potential cytotoxic effects. We interrogated assembly in mammalian cells by using the WRB/CAML complex, an essential insertase for tail-anchored proteins in the endoplasmic reticulum (ER), as a model system. Our data suggest that the stability of each subunit is differentially regulated. In WRB's absence, CAML folds incorrectly, causing aberrant exposure of a hydrophobic transmembrane domain to the ER lumen. When present, WRB can correct the topology of CAML both in vitro and in cells. In contrast, WRB can independently fold correctly but is still degraded in the absence of CAML. We therefore propose that there are at least two distinct regulatory pathways for the surveillance of orphan subunits in the mammalian ER.

Keywords: endoplasmic reticulum; membrane proteins; oligomeric assembly; quality control.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adaptor Proteins, Signal Transducing / metabolism*
  • Animals
  • Dogs
  • Endoplasmic Reticulum / metabolism
  • HEK293 Cells
  • Humans
  • Multiprotein Complexes / metabolism*
  • Nuclear Proteins / metabolism*
  • Protein Binding
  • Protein Stability
  • Protein Subunits / metabolism*
  • Proteolysis
  • Rabbits
  • Ribosomes / metabolism

Substances

  • Adaptor Proteins, Signal Transducing
  • Multiprotein Complexes
  • Nuclear Proteins
  • Protein Subunits