Simultaneous Control of Endogenous and User-Defined Genetic Pathways Using Unique ecDHFR Pharmacological Chaperones

Cell Chem Biol. 2020 May 21;27(5):622-634.e6. doi: 10.1016/j.chembiol.2020.03.006. Epub 2020 Apr 23.

Abstract

Destabilizing domains (DDs), such as a mutated form of Escherichia coli dihydrofolate reductase (ecDHFR), confer instability and promote protein degradation. However, when combined with small-molecule stabilizers (e.g., the antibiotic trimethoprim), DDs allow positive regulation of fusion protein abundance. Using a combinatorial screening approach, we identified and validated 17 unique 2,4-diaminopyrimidine/triazine-based ecDHFR DD stabilizers, at least 15 of which were ineffective antibiotics against E. coli and S. aureus. Identified stabilizers functioned in vivo to control an ecDHFR DD-firefly luciferase in the mouse eye and/or the liver. Next, stabilizers were leveraged to perform synergistic dual functions in vitro (HeLa cell death sensitization) and in vivo (repression of ocular inflammation) by stabilizing a user-defined ecDHFR DD while also controlling endogenous signaling pathways. Thus, these newly identified pharmacological chaperones allow for simultaneous control of compound-specific endogenous and user-defined genetic pathways, the combination of which may provide synergistic effects in complex biological scenarios.

Keywords: E. coli dihydrofolate reductase; chemical biology; conditional regulation; destabilizing domain; dual use; gene therapy; high-throughput screening; ocular; pharmacological chaperone.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • Anti-Bacterial Agents / chemistry
  • Anti-Bacterial Agents / pharmacology*
  • Enzyme Inhibitors / chemistry
  • Enzyme Inhibitors / pharmacology
  • Enzyme Stability / drug effects*
  • Escherichia coli / enzymology
  • Female
  • Folic Acid Antagonists / chemistry
  • Folic Acid Antagonists / pharmacology*
  • HeLa Cells
  • Humans
  • Male
  • Mice
  • Mice, Inbred BALB C
  • Pyrimidines / chemistry
  • Pyrimidines / pharmacology*
  • Tetrahydrofolate Dehydrogenase / chemistry
  • Tetrahydrofolate Dehydrogenase / metabolism*
  • Triazines / chemistry
  • Triazines / pharmacology
  • Trimethoprim / analogs & derivatives
  • Trimethoprim / pharmacology

Substances

  • Anti-Bacterial Agents
  • Enzyme Inhibitors
  • Folic Acid Antagonists
  • Pyrimidines
  • Triazines
  • 2,4-diaminopyrimidine
  • Trimethoprim
  • Tetrahydrofolate Dehydrogenase