Left ventricular non compaction and septal defects

Tunis Med. 2020 Feb;98(2):161-163.

Abstract

We report the case of a 23-year-old woman with a not yet described (to the best of our knowledge) association of left ventricle non-compaction with both atrial and ventricular defects. Family genetic survey concluded to, a probably sporadic, E101K gene mutation.

Publication types

  • Case Reports

MeSH terms

  • Amino Acid Substitution / genetics
  • Dystrophin-Associated Proteins / genetics
  • Female
  • Glutamic Acid / genetics
  • Heart Defects, Congenital / diagnosis*
  • Heart Defects, Congenital / genetics
  • Heart Septal Defects, Atrial / complications
  • Heart Septal Defects, Atrial / diagnosis*
  • Heart Septal Defects, Atrial / genetics
  • Heart Ventricles / abnormalities*
  • Humans
  • Lysine / genetics
  • Mutation, Missense
  • Neuropeptides / genetics
  • Young Adult

Substances

  • DTNA protein, human
  • Dystrophin-Associated Proteins
  • Neuropeptides
  • Glutamic Acid
  • Lysine

Supplementary concepts

  • Noncompaction of Left Ventricular Myocardium with Congenital Heart Defects