Vasoocclusion with homozygous hemoglobin-C disease

Am J Pediatr Hematol Oncol. 1988 Winter;10(4):323-5. doi: 10.1097/00043426-198824000-00011.

Abstract

Hemoglobin-CC is a relatively uncommon hemoglobinopathy, seen primarily in the black population. These patients usually have a mild clinical course, without significant risk of vasoocclusive crises. There are no routine recommendations for preparation prior to surgery. We present a patient who developed a clinical picture suggestive of major vasoocclusion after cardiac by-pass surgery. In retrospect, these signs appear to be the result of hemodynamic instability and cardiogenic shock instead of vasoocclusion.

Publication types

  • Case Reports

MeSH terms

  • Aortic Valve Stenosis / surgery
  • Cardiopulmonary Bypass / adverse effects*
  • Child
  • Exchange Transfusion, Whole Blood
  • Hemoglobin C Disease / complications*
  • Humans
  • Male
  • Thrombosis / etiology*