Mthfd2 Modulates Mitochondrial Function and DNA Repair to Maintain the Pluripotency of Mouse Stem Cells

Stem Cell Reports. 2020 Aug 11;15(2):529-545. doi: 10.1016/j.stemcr.2020.06.018. Epub 2020 Jul 16.

Abstract

The pluripotency of stem cells determines their developmental potential. While the pluripotency states of pluripotent stem cells are variable and interconvertible, the mechanisms underlying the acquisition and maintenance of pluripotency remain largely elusive. Here, we identified that methylenetetrahydrofolate dehydrogenase (NAD+-dependent), methenyltetrahydrofolate cyclohydrolase (Mthfd2) plays an essential role in maintaining embryonic stem cell pluripotency and promoting complete reprogramming of induced pluripotent stem cells. Mechanistically, in mitochondria, Mthfd2 maintains the integrity of the mitochondrial respiratory chain and prevents mitochondrial dysfunction. In the nucleus, Mthfd2 stabilizes the phosphorylation of EXO1 to support DNA end resection and promote homologous recombination repair. Our results revealed that Mthfd2 is a dual-function factor in determining the pluripotency of pluripotent stem cells through both mitochondrial and nuclear pathways, ultimately ensuring safe application of pluripotent stem cells.

Keywords: DNA repair; Mthfd2; mitochondrial dysfunction; pluripotency; pluripotent stem cells.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Aminohydrolases / metabolism*
  • Animals
  • CDC2 Protein Kinase / metabolism
  • Cell Nucleus / metabolism
  • Cell Self Renewal / genetics
  • DNA Damage
  • DNA Repair Enzymes / metabolism
  • DNA Repair*
  • Electron Transport Complex III / metabolism
  • Exodeoxyribonucleases / metabolism
  • Gene Expression Regulation
  • Glucose / metabolism
  • Glycolysis
  • Induced Pluripotent Stem Cells / metabolism*
  • Methenyltetrahydrofolate Cyclohydrolase / deficiency
  • Methenyltetrahydrofolate Cyclohydrolase / metabolism*
  • Methylenetetrahydrofolate Dehydrogenase (NADP) / metabolism*
  • Mice
  • Mitochondria / metabolism*
  • Mouse Embryonic Stem Cells / metabolism
  • Multienzyme Complexes / metabolism*
  • Oxidative Phosphorylation
  • Phosphorylation
  • Protein Binding

Substances

  • Multienzyme Complexes
  • UQCRC2 protein, mouse
  • methylene tetrahydrofolate dehydrogenase-methenyltetrahydrofolate cyclohydrolase
  • Methylenetetrahydrofolate Dehydrogenase (NADP)
  • CDC2 Protein Kinase
  • Cdk1 protein, mouse
  • Exo1 protein, mouse
  • Exodeoxyribonucleases
  • Aminohydrolases
  • Methenyltetrahydrofolate Cyclohydrolase
  • DNA Repair Enzymes
  • Electron Transport Complex III
  • Glucose