A rare case of MGRS with immunotactoid glomerulopathy responding to bortezomib, dexamethasone, and rituximab

Chaoyuan Kuang; Kevin Quann; Agnes K Liman; Roy Frye; Nawras Alshoubaki; Mohan Ramkumar; Andrew D Liman

doi:10.1002/ccr3.3044

A rare case of MGRS with immunotactoid glomerulopathy responding to bortezomib, dexamethasone, and rituximab

Clin Case Rep. 2020 Jun 22;8(10):1984-1987. doi: 10.1002/ccr3.3044. eCollection 2020 Oct.

Authors

Chaoyuan Kuang^{1

2}, Kevin Quann^{1

2}, Agnes K Liman³, Roy Frye³, Nawras Alshoubaki⁴, Mohan Ramkumar⁴, Andrew D Liman¹

Affiliations

¹ Hematology/Oncology section VA Pittsburgh Healthcare System Pittsburgh PA USA.
² UPMC Hillman Cancer Center Pittsburgh PA USA.
³ Pathology and Laboratory Medicine VA Pittsburgh Healthcare System Pittsburgh PA USA.
⁴ Renal section VA Pittsburgh Healthcare System Pittsburgh PA USA.

Abstract

Patients with monoclonal gammopathy of renal significance should be treated with clone-directed therapy against sources of monoclonal proteins in order to prevent progression to more advanced monoclonal gammopathies and renal failure.

Keywords: Waldenstrom's macroglobulinemia; immunotactoid glomerulopathy; monoclonal gammopathy of renal significance; nephrotic syndrome.

Publication types

Case Reports