Sprengel Deformity with Omovertebral Bone Encroaching the Spinal Canal Causing Progressive Cervical Myelopathy: A Technical Case Report

World Neurosurg. 2021 Feb:146:163-165. doi: 10.1016/j.wneu.2020.11.070. Epub 2020 Nov 18.

Abstract

An adult with Sprengel deformity and Klippel-Feil syndrome associated with an omovertebral bone has rarely been reported in literature. The omovertebral bone is an abnormal cartilaginous connection between the scapula and the cervical spine. Limited cases have previously been reported in the literature describing surgical intervention when neurologic deficits such as cervical myelopathy or radiculopathy are present. In the present case, an omovertebral bone extended into the cervical lamina resulting in cervical myeloradiculopathy requiring resection of the bony anomaly and cervicothoracic fusion. The omovertebral bone as an etiology for radiculopathy or myelopathy is rarely seen in an adult population, and surgical decompression and fusion should be considered with this constellation of anomalies.

Keywords: Cervical fusion; Compressive myelopathy; Klippel-Feil syndrome; Sprengel deformity.

Publication types

  • Case Reports

MeSH terms

  • Cervical Cord / pathology
  • Cervical Vertebrae / abnormalities*
  • Cervical Vertebrae / surgery
  • Congenital Abnormalities
  • Female
  • Humans
  • Klippel-Feil Syndrome / complications*
  • Middle Aged
  • Scapula / abnormalities*
  • Scapula / surgery
  • Shoulder Joint / abnormalities*
  • Spinal Cord Diseases / etiology*
  • Spinal Cord Diseases / surgery
  • Spinal Fusion / methods

Supplementary concepts

  • Sprengel deformity