Trisomy 8 mosaicism in the placenta: A Danish cohort study of 37 cases and a literature review

Prenat Diagn. 2021 Mar;41(4):409-421. doi: 10.1002/pd.5875. Epub 2020 Dec 18.

Abstract

Objective: To evaluate the risk of fetal involvement when trisomy 8 mosaicism (T8M) is detected in chorionic villus samples (CVS).

Methods: A retrospective descriptive study of registered pregnancies in Denmark with T8M in CVS identified through a database search and a review of published cases of T8M found through a systematic literature search and inclusion of cross references. Pregnancies with T8M in CVS and no additional numerical chromosomal aberrations were included.

Results: A total of 37 Danish cases and 60 published cases were included. T8M detected in a CVS was associated with fetal involvement in 18 out of 97 pregnancies (18.6% [95%CI: 11.4-27.7]). Eight out of 70 (11.4% [95%CI: 5.1-21.3]) interpreted prenatally to be confined placental mosaicism (CPM) were subsequently found to be true fetal mosaicisms (TFM).

Conclusion: T8M detected in CVS poses a significant risk of fetal involvement, and examination of amniotic fluid (AF) and/or fetal tissue should be offered. However, a normal result of AF still has a considerable residual risk of fetal involvement. Genetic counselling at an early gestational age is essential, and follow-up ultrasonography should be performed to predict fetal involvement if possible.

Publication types

  • Review

MeSH terms

  • Adult
  • Chorionic Villi Sampling / methods
  • Chromosomes, Human, Pair 8
  • Cohort Studies
  • Denmark / epidemiology
  • Female
  • Humans
  • Mosaicism
  • Placenta / abnormalities
  • Placenta / physiopathology*
  • Pregnancy
  • Registries / statistics & numerical data
  • Retrospective Studies
  • Trisomy / diagnosis*
  • Trisomy / physiopathology
  • Uniparental Disomy / diagnosis*
  • Uniparental Disomy / physiopathology

Supplementary concepts

  • Chromosome 8, mosaic trisomy