Aortopulmonary window with anomalous origin of the right coronary artery from the pulmonary trunk

Cardiol Young. 2021 May;31(5):838-841. doi: 10.1017/S1047951120004783. Epub 2021 Jan 11.

Abstract

Anomalous origin of coronary artery originating from the pulmonary artery in conjunction with the aorticopulmonary window (APW) is a rare but a significant anomaly in the era of congenital cardiac diseases. The occurrence of anomalous origin of the right coronary artery from the pulmonary artery among the associated anomalies is less than 5%. The severity of the clinical condition of these patients depends on the degree of left-right shunt and compromise of the pulmonary blood flow. We report surgical management of a case of a 45-day-old infant with APW, ventricular septal defect, and anomalous origin of coronary artery originated from the pulmonary artery.

Keywords: ARCAPA; Aortopulmonary window; congenital cardiac surgery.

Publication types

  • Case Reports

MeSH terms

  • Aortopulmonary Septal Defect* / diagnostic imaging
  • Aortopulmonary Septal Defect* / surgery
  • Coronary Vessel Anomalies* / diagnostic imaging
  • Coronary Vessel Anomalies* / surgery
  • Humans
  • Infant
  • Pulmonary Artery / diagnostic imaging
  • Pulmonary Artery / surgery
  • Pulmonary Circulation