A Rare Variant of Hypogenetic Lung Syndrome Mimicking Scimitar Vein

Tommaso D'Angelo; Alfredo Blandino; Michele B Saitta; Salvatore Agati; Placido Romeo; Silvio Mazziotti

doi:10.1016/j.athoracsur.2021.01.020

A Rare Variant of Hypogenetic Lung Syndrome Mimicking Scimitar Vein

Ann Thorac Surg. 2021 Sep;112(3):e173-e176. doi: 10.1016/j.athoracsur.2021.01.020. Epub 2021 Jan 23.

Authors

Tommaso D'Angelo¹, Alfredo Blandino², Michele B Saitta³, Salvatore Agati³, Placido Romeo⁴, Silvio Mazziotti²

Affiliations

¹ Section of Radiology, Department of Biomedical Sciences and Morphological and Functional Imaging, G. Martino University Hospital Messina, Messina, Italy. Electronic address: [email protected].
² Section of Radiology, Department of Biomedical Sciences and Morphological and Functional Imaging, G. Martino University Hospital Messina, Messina, Italy.
³ Mediterranean Pediatric Cardiology Center, Bambino Gesù Children's Hospital, Taormina, Italy.
⁴ Department of Radiology, S. Vincenzo Hospital, Taormina, Italy.

PMID: 33497669
DOI: 10.1016/j.athoracsur.2021.01.020

Abstract

Hypogenetic lung syndrome, also known as scimitar syndrome, is a rare and well-known congenital condition that includes hypoplastic right pulmonary artery and lung, right displacement of the heart, anomalous systemic arterial supply to the lung, and a characteristically curved anomalous right pulmonary vein draining into the inferior vena cava. In exceptional cases, the anomalous pulmonary vein may drain into left atrium. We here report a case of a 17-year-old girl with a rare variant of hypogenetic lung syndrome diagnosed by means of multimodality imaging and treated with percutaneous occlusion of the aortopulmonary collateral.

Publication types

Case Reports

MeSH terms

Abnormalities, Multiple / diagnosis*
Adolescent
Diagnosis, Differential
Female
Heart Atria / abnormalities*
Humans
Pulmonary Veins / abnormalities*
Scimitar Syndrome / classification*
Scimitar Syndrome / diagnosis*
Vena Cava, Inferior / abnormalities*