Dipeptidyl peptidase 9 sets a threshold for CARD8 inflammasome formation by sequestering its active C-terminal fragment

Immunity. 2021 Jul 13;54(7):1392-1404.e10. doi: 10.1016/j.immuni.2021.04.024. Epub 2021 May 20.

Abstract

CARD8 detects intracellular danger signals and forms a caspase-1 activating inflammasome. Like the related inflammasome sensor NLRP1, CARD8 autoprocesses into noncovalently associated N-terminal (NT) and C-terminal (CT) fragments and binds the cellular dipeptidyl peptidases DPP8 and 9 (DPP8/9). Certain danger-associated signals, including the DPP8/9 inhibitor Val-boroPro (VbP) and HIV protease, induce proteasome-mediated NT degradation and thereby liberate the inflammasome-forming CT. Here, we report cryoelectron microscopy (cryo-EM) structures of CARD8 bound to DPP9, revealing a repressive ternary complex consisting of DPP9, full-length CARD8, and CARD8-CT. Unlike NLRP1-CT, CARD8-CT does not interact with the DPP8/9 active site and is not directly displaced by VbP. However, larger DPP8/9 active-site probes can directly weaken this complex in vitro, and VbP itself nevertheless appears to disrupt this complex, perhaps indirectly, in cells. Thus, DPP8/9 inhibitors can activate the CARD8 inflammasome by promoting CARD8 NT degradation and by weakening ternary complex stability.

Keywords: CARD8; DPP9; NLRP1; Val-boroPro (VbP); cryo-EM; inflammasome; pyroptosis; targeted degradation.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, U.S. Gov't, Non-P.H.S.

MeSH terms

  • Animals
  • CARD Signaling Adaptor Proteins / metabolism*
  • Caspase 1 / metabolism
  • Catalytic Domain / physiology
  • Cell Line
  • Cryoelectron Microscopy / methods
  • Dipeptidyl-Peptidases and Tripeptidyl-Peptidases / metabolism*
  • HEK293 Cells
  • Humans
  • Inflammasomes / metabolism*
  • Neoplasm Proteins / metabolism*
  • Proteolysis
  • Sf9 Cells

Substances

  • CARD Signaling Adaptor Proteins
  • CARD8 protein, human
  • Inflammasomes
  • Neoplasm Proteins
  • DPP9 protein, human
  • Dipeptidyl-Peptidases and Tripeptidyl-Peptidases
  • Caspase 1