Posterior Cloacal Variant with Clitorolabial Transposition and a Rectoperineal Fistula

European J Pediatr Surg Rep. 2021 Jan;9(1):e46-e49. doi: 10.1055/s-0041-1728724. Epub 2021 May 18.

Abstract

We present a case and discuss the management of a posterior cloacal variant not as yet described in the literature. A 5-week-old infant presented to our institution with a posterior cloacal variant and transposition of the clitoris and labia. After initial radiological investigations, staged operative intervention was performed over a 1-year period. This included an initial laparotomy (with drainage of hydrocolpos and formation of a colostomy), a left ureteric reimplantation and a posterior sagittal anorectoplasty due to a rectoperineal fistula. The child is under continued long-term follow-up by our specialist pediatric surgical team.

Keywords: anorectal malformation; cloaca; posterior cloacal variant.

Publication types

  • Case Reports