Estimating the health benefits of timely diagnosis and treatment of transthyretin amyloid cardiomyopathy

J Comp Eff Res. 2021 Aug;10(11):927-938. doi: 10.2217/cer-2021-0071. Epub 2021 Jun 18.

Abstract

Aim: Delayed diagnosis of transthyretin amyloid cardiomyopathy (ATTR-CM) represents a missed opportunity for intervention. This study estimates the health benefits of timely diagnosis and treatment with tafamidis. Methods: A disease simulation model was developed to predict health outcomes under scenarios of timely and delayed diagnosis and treatment. Efficacy and quality of life (QoL) profiles were derived from the pivotal tafamidis trial and diagnostic delay durations from the literature. Results: Timely diagnosis and treatment were predicted to extend mean life expectancy by 5.46 and 7.76 years, relative to delayed diagnosis, for wild-type and hereditary ATTR-CM, respectively. Corresponding QALY gains were 4.50 and 6.22. Conclusion: Timely diagnosis and treatment with tafamidis are predicted to significantly improve survival and QoL for ATTR-CM patients.

Keywords: ATTR-CM; diagnosis; disease simulation model; health outcomes; tafamidis; transthyretin amyloid cardiomyopathy.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Amyloid Neuropathies, Familial* / diagnosis
  • Amyloid Neuropathies, Familial* / drug therapy
  • Amyloid Neuropathies, Familial* / genetics
  • Cardiomyopathies* / diagnosis
  • Cardiomyopathies* / drug therapy
  • Delayed Diagnosis
  • Humans
  • Prealbumin / genetics
  • Quality of Life

Substances

  • Prealbumin