Enterovirus A71 causing meningoencephalitis and acute flaccid myelitis in a patient receiving rituximab

J Neuroimmunol. 2021 Sep 15:358:577639. doi: 10.1016/j.jneuroim.2021.577639. Epub 2021 Jun 24.

Abstract

We present the case of a young woman being treated with rituximab for rheumatoid arthritis who developed a severe enteroviral meningoencephalitis and acute flaccid myelitis (AFM). Cerebrospinal fluid (CSF) and stool reverse transcription-polymerase chain reaction (RT-PCR) testing confirmed the diagnosis and additional sequencing studies performed at the CDC further characterized the enterovirus as enterovirus A71 (EV-A71). After treatment with intravenous immunoglobulin (IVIg) and fluoxetine (based on previous reports of possible efficacy) the patient experienced a remarkable improvement over time. This case highlights the importance of considering enteroviral infection in patients treated with rituximab, depicts a possible clinical course of enteroviral meningoencephalitis and AFM, and illustrates the importance of testing multiple sites for enterovirus infection (CSF, stool, nasopharyngeal swab, blood). Here we present the case with a brief review of the literature pertaining to EV-A71.

Keywords: AFM; Acute flaccid myelitis; Acute flaccid paralysis; Encephalitis; Enterovirus; Enterovirus A71; Meningitis; Meningoencephalitis; Poliomyelitis; Rheumatoid arthritis; Rituximab.

Publication types

  • Case Reports
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adult
  • Central Nervous System Viral Diseases / diagnostic imaging*
  • Central Nervous System Viral Diseases / drug therapy
  • Central Nervous System Viral Diseases / virology
  • Enterovirus A, Human / isolation & purification*
  • Enterovirus Infections / diagnostic imaging*
  • Enterovirus Infections / drug therapy
  • Female
  • Humans
  • Immunologic Factors / adverse effects
  • Immunologic Factors / therapeutic use*
  • Meningoencephalitis / diagnostic imaging*
  • Meningoencephalitis / drug therapy
  • Meningoencephalitis / virology
  • Myelitis / diagnostic imaging*
  • Myelitis / drug therapy
  • Myelitis / virology
  • Neuromuscular Diseases / diagnostic imaging*
  • Neuromuscular Diseases / drug therapy
  • Neuromuscular Diseases / virology
  • Rituximab / adverse effects
  • Rituximab / therapeutic use*

Substances

  • Immunologic Factors
  • Rituximab

Supplementary concepts

  • acute flaccid myelitis