Macrophage Activation Syndrome in a Patient with Prolidase Deficiency: a Rare Genetic Disorder Associated with Elevated IgE and Lupus-Like Syndrome

J Clin Immunol. 2021 Oct;41(7):1696-1700. doi: 10.1007/s10875-021-01096-2. Epub 2021 Jul 15.

Authors

Aakash Chandran Chidambaram¹, Santhosh Kumar Thangaraju¹, Sanjana Sarangarajan¹, Kaushik Maulik¹, Jaikumar Govindaswamy Ramamoorthy², Dhandapany Gunasekaran¹

Affiliations

¹ Department of Pediatrics, Jawaharlal Institute of Postgraduate Medical Education and Research (JIPMER), Puducherry, 605006, India.
² Department of Pediatrics, Jawaharlal Institute of Postgraduate Medical Education and Research (JIPMER), Puducherry, 605006, India. [email protected].

PMID: 34263393
DOI: 10.1007/s10875-021-01096-2

No abstract available

Publication types

Case Reports
Letter

MeSH terms

Child
Female
Humans
Immunoglobulin E / blood*
Lupus Erythematosus, Systemic / blood
Macrophage Activation Syndrome* / blood
Prolidase Deficiency* / blood
Syndrome

Substances

Immunoglobulin E