This International evidence-based nomenclature and classification consensus on the congenital bicuspid aortic valve and its aortopathy recognizes 3 types of bicuspid aortic valve: 1. Fused type, with 3 phenotypes: right-left cusp fusion, right-non cusp fusion and left-non cusp fusion; 2. 2-sinus type with 2 phenotypes: Latero-lateral and antero-posterior; and 3. Partial-fusion or forme fruste. This consensus recognizes 3 bicuspid-aortopathy types: 1. Ascending phenotype; root phenotype; and 3. extended phenotypes.
Keywords: Aortopathy; Bicuspid aortic valve; Classification; Nomenclature.
This article has been co-published with permission in the European Journal of Cardio-Thoracic Surgery, The Annals of Thoracic Surgery, the Journal of Thoracic and Cardiovascular Surgery, and in Radiology: Cardiothoracic Imaging. All rights reserved. © 2021 Jointly between the European Association for Cardio-Thoracic Surgery, The Society of Thoracic Surgeons, the American Association for Thoracic Surgery, and the Radiological Society of North America. The articles are identical except for minor stylistic and spelling differences in keeping with each journal’s style.