Reports of 2 Rare Associations of Hypoplastic Left Heart Syndrome

K Anitha Jayakumar; Gouri Tilak; Bibhuti B Das

doi:10.1016/j.jaccas.2019.10.025

Reports of 2 Rare Associations of Hypoplastic Left Heart Syndrome

JACC Case Rep. 2019 Dec 18;1(4):526-531. doi: 10.1016/j.jaccas.2019.10.025. eCollection 2019 Dec.

Authors

K Anitha Jayakumar¹, Gouri Tilak², Bibhuti B Das¹

Affiliations

¹ Pediatric Heart Institute, Joe DiMaggio Children's Hospital, Hollywood, Florida.
² Department of Radiology, Joe DiMaggio Children's Hospital, Hollywood, Florida.

Abstract

This report describes 2 contrasting yet rare associations of hypoplastic left heart syndrome, 1 in a patient with pulmonary valve stenosis that was successfully surgically palliated and the other in a patient with an intact atrial septum and stenotic bilateral levoatriocardinal veins who was offered comfort care. These cases underscore the point that although both infants were born with hypoplastic left heart syndrome, the outcomes can dramatically differ as a result of anatomic and physiological variables. (Level of Difficulty: Advanced.).

Keywords: CHD, congenital heart disease; HLHS, hypoplastic left heart syndrome; IUGR, intrauterine growth retardation; PA, pulmonary artery; congenital heart disease; hypoplastic left heart syndrome; levoatriocardinal veins; palliative care; pulmonary valve dysplasia.

Publication types

Case Reports