Pulmonary Atresia With Ventriculocoronary Arterial Connections and a Large Conoventricular Septal Defect

Réda Jakamy; Pierre-Emmanuel Séguéla; Estibaliz Valdeolmillos; Mansour Mostefa Kara; Jean-Baptiste Mouton; Xavier Iriart; Jean-Benoit Thambo

doi:10.1016/j.jaccas.2019.09.008

Pulmonary Atresia With Ventriculocoronary Arterial Connections and a Large Conoventricular Septal Defect

JACC Case Rep. 2019 Oct 30;1(4):545-548. doi: 10.1016/j.jaccas.2019.09.008. eCollection 2019 Dec.

Authors

Réda Jakamy¹, Pierre-Emmanuel Séguéla¹, Estibaliz Valdeolmillos¹, Mansour Mostefa Kara¹, Jean-Baptiste Mouton¹, Xavier Iriart¹, Jean-Benoit Thambo¹

Affiliation

¹ Department of Pediatric and Adult Congenital Heart Disease, Haut-Lévêque Cardiology Hospital, M3C National Reference Centre, University Hospital of Bordeaux, Bordeaux-Pessac, France.

Abstract

Ventriculocoronary arterial connections are typically found in patients with pulmonary atresia with an intact ventricular septum. This report describes a case of ventriculocoronary arterial connections in a patient with pulmonary atresia with a ventricular septal defect. Our case supports recent data suggesting a primary coronary artery developmental anomaly in pulmonary atresia. (Level of Difficulty: Advanced.).

Keywords: PA-IVS, pulmonary atresia with intact ventricular septum; PA-VSD, pulmonary atresia with ventricular septal defect; VCAC, ventriculocoronary arterial connection; VSD, ventricular septal defect; congenital heart defect; coronary circulation; coronary vessel anomaly; pulmonary atresia; right ventricle; ventricular septal defect.

Publication types

Case Reports