Isolated Antineutrophil Cytoplasmic Antibody-Associated Coronary Vasculitis and Valvulitis

Yoon Kook Kim; Praveen Chekka; Manu Mysore; James Childress; Maha Alfaraidhy; Afton Thomas; Bradley Taylor; Jamal Mikdashi; Stanley Liu; Libin Wang

doi:10.1016/j.jaccas.2020.12.007

Isolated Antineutrophil Cytoplasmic Antibody-Associated Coronary Vasculitis and Valvulitis

JACC Case Rep. 2021 Feb 10;3(2):309-313. doi: 10.1016/j.jaccas.2020.12.007. eCollection 2021 Feb.

Authors

Affiliation

¹ Department of Medicine, University of Maryland School of Medicine, Baltimore, Maryland, USA.

Abstract

A 30-year-old woman presented with angina pectoris. Coronary angiography revealed severe stenosis in the left main and right coronary arteries that did not improve with intracoronary nitroglycerin. Coronary computed tomography angiography and positron emission tomography revealed coronary ostia inflammation and aortic root fat stranding. She was diagnosed with vasculitis and valvulitis and received immunotherapy and coronary bypass. (Level of Difficulty: Advanced.).

Keywords: AAV, ANCA associated vasculitis; ANCA, antineutrophil cytoplasmic antibody; CABG, coronary artery bypass grafting; CTA, computed tomography angiography; FDG, fluorodeoxyglucose; LMCA, left main coronary artery; MPA, microscopic polyangiitis; MRA, magnetic resonance angiography; PET, positron emission tomography; RCA, right coronary artery; aortic valve; autoimmune; coronary artery bypass; vascular disease.

Publication types

Case Reports