Pentalogy of Cantrell With a Left Ventricular Diverticulum and Muscular VSD

Morgan Ashley Hill; Jennie H Kwon; T Konrad Rajab; Minoo N Kavarana

doi:10.1016/j.athoracsur.2021.07.093

Pentalogy of Cantrell With a Left Ventricular Diverticulum and Muscular VSD

Ann Thorac Surg. 2022 Jun;113(6):e461-e463. doi: 10.1016/j.athoracsur.2021.07.093. Epub 2021 Sep 2.

Authors

Morgan Ashley Hill¹, Jennie H Kwon¹, T Konrad Rajab¹, Minoo N Kavarana²

Affiliations

¹ Section of Pediatric Cardiothoracic Surgery, Department of Surgery, Medical University of South Carolina, Charleston, South Carolina.
² Section of Pediatric Cardiothoracic Surgery, Department of Surgery, Medical University of South Carolina, Charleston, South Carolina. Electronic address: [email protected].

PMID: 34481798
DOI: 10.1016/j.athoracsur.2021.07.093

Abstract

Pentalogy of Cantrell (POC) is a rare congenital disorder characterized by defects of the anterior diaphragm, midline supraumbilical abdominal wall, diaphragmatic pericardium, lower sternum, and heart. The low incidence and significant heterogeneity of POC make it difficult for most surgeons to gain consistent experience in treating these congenital heart defects. Here, we describe the treatment of a patient with POC, tetralogy of Fallot, left ventricular diverticulum, and a muscular ventricular septal defect. An innovative approach through a left ventricular diverticulotomy was utilized, which provided excellent exposure for repair of the muscular ventricular septal defect.

Publication types

Case Reports

MeSH terms

Abdominal Wall* / abnormalities
Diverticulum* / diagnosis
Diverticulum* / diagnostic imaging
Heart Defects, Congenital* / surgery
Heart Septal Defects, Ventricular* / complications
Heart Septal Defects, Ventricular* / diagnostic imaging
Heart Septal Defects, Ventricular* / surgery
Humans
Pentalogy of Cantrell* / diagnosis
Pentalogy of Cantrell* / surgery