Abstract
We studied two patients with nonfamilial olivopontocerebellar atrophy with skeletal myoclonus. Palatal or skeletal myoclonus is probably not a coincidental finding but another manifestation of the underlying disease. In both cases, the myoclonus was suppressed by administration of trihexyphenidyl, indicating a cholinergic disorder.
MeSH terms
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Brain / diagnostic imaging
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Clonazepam / therapeutic use
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Drug Therapy, Combination
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Electromyography
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Female
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Humans
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Male
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Middle Aged
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Muscles / physiopathology
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Myoclonus / drug therapy*
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Myoclonus / etiology
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Myoclonus / physiopathology
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Olivopontocerebellar Atrophies / complications*
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Olivopontocerebellar Atrophies / diagnostic imaging
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Spinocerebellar Degenerations / complications*
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Tomography, X-Ray Computed
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Trihexyphenidyl / therapeutic use*
Substances
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Clonazepam
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Trihexyphenidyl