The Lysosomal Rag-Ragulator Complex Licenses RIPK1 and Caspase-8-mediated Pyroptosis by Yersinia

Science. 2021 Jun 25;372(6549):eabg0269. doi: 10.1126/science.abg0269.

Abstract

Host cells initiate cell death programs to limit pathogen infection. Inhibition of transforming growth factor-β-activated kinase 1 (TAK1) by pathogenic Yersinia in macrophages triggers receptor-interacting serine/threonine-protein kinase 1 (RIPK1)-dependent caspase-8 cleavage of gasdermin D (GSDMD) and inflammatory cell death (pyroptosis). A genome-wide clustered regularly interspaced short palindromic repeats (CRISPR) screen to uncover mediators of caspase-8-dependent pyroptosis identified an unexpected role of the lysosomal FLCN-FNIP2-Rag-Ragulator supercomplex, which regulates metabolic signalling and the mechanistic target of rapamycin complex 1 (mTORC1). In response to Yersinia infection, FADD, RIPK1 and caspase-8 were recruited to Rag-Ragulator, causing RIPK1 phosphorylation and caspase-8 activation. Pyroptosis activation depended on Rag GTPase activity and lysosomal tethering of Rag-Ragulator, but not mTORC1. Thus, the lysosomal metabolic regulator Rag-Ragulator instructs the inflammatory response to Yersinia.

Publication types

  • Research Support, N.I.H., Extramural
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Animals
  • CRISPR-Cas Systems
  • Caspase 8 / metabolism*
  • Cells, Cultured
  • HEK293 Cells
  • Humans
  • Inflammasomes / metabolism
  • Intracellular Membranes / metabolism
  • Lysosomes / metabolism*
  • MAP Kinase Kinase Kinases / antagonists & inhibitors
  • MAP Kinase Kinase Kinases / metabolism
  • Macrophages / metabolism*
  • Macrophages / microbiology*
  • Mice
  • Monomeric GTP-Binding Proteins / metabolism
  • Multiprotein Complexes / metabolism
  • Pyroptosis*
  • Receptor-Interacting Protein Serine-Threonine Kinases / metabolism*
  • Signal Transduction
  • Yersinia pseudotuberculosis / pathogenicity
  • Yersinia pseudotuberculosis / physiology*

Substances

  • Inflammasomes
  • Multiprotein Complexes
  • Receptor-Interacting Protein Serine-Threonine Kinases
  • Ripk1 protein, mouse
  • MAP Kinase Kinase Kinases
  • MAP kinase kinase kinase 7
  • Casp8 protein, mouse
  • Caspase 8
  • Monomeric GTP-Binding Proteins