Molecular characterization and reclassification of a 1.18 Mbp DMD duplication following positive carrier screening for Duchenne/Becker muscular dystrophy

Clin Case Rep. 2022 Jul 11;10(7):e6008. doi: 10.1002/ccr3.6008. eCollection 2022 Jul.

Abstract

A 2-month-old male patient harboring a duplication of DMD exons 1-7 classified as pathogenic by an outside institution presented with mildly elevated creatine phosphokinase (CK); molecular breakpoint analysis by our laboratory reclassified the duplication as likely benign. To date, proband continues to develop normally with decreased CK, further supporting our reclassification.

Keywords: DMD; Duchenne muscular dystrophy; duplication; dystrophinopathy.

Publication types

  • Case Reports