Endovascular management of a congenital hepatic arterioportal malformation in a low resource setting

Poonamjeet Loyal; Ravjit Sagoo

doi:10.1186/s42155-022-00314-1

Endovascular management of a congenital hepatic arterioportal malformation in a low resource setting

CVIR Endovasc. 2022 Aug 6;5(1):38. doi: 10.1186/s42155-022-00314-1.

Authors

Poonamjeet Loyal¹, Ravjit Sagoo²

Affiliations

¹ Radiology Department, Aga Khan University Hospital Nairobi, P.O. BOX 30270, Nairobi, 00100, Kenya. [email protected].
² Radiology Department, Aga Khan University Hospital Nairobi, Nairobi, Kenya.

Abstract

Background: Arterioportal malformations, a rare type of vascular malformation, have significant associated morbidity and mortality. Management requires a carefully thought out approach by a multidisciplinary team. Low resource settings have an added challenge of limited treatment options and consumables.

Case presentation: We report a case of a 14-month-old male with failure to thrive due to a congenital hepatic arterioportal fistula. He was successfully treated via an endovascular approach with metallic coil embolization.

Conclusion: Hepatoportal fistula, a rare hepatic vascular malformation, has limited treatment options which can further be restricted by overall patient wellness. Minimally invasive endovascular treatment options can offer a high rate of success and reverse the morbidity associated with the disease as was seen with our case.

Keywords: Congenital hepatic arterioportal fistula; Metallic coil embolization.