A rare case report of multifocal para-aortic and para-vesical paragangliomas

San-Chao Xiong; Xing-Peng Di; Meng-Ni Zhang; Kan Wu; Xiang Li

doi:10.3389/fendo.2022.946496

A rare case report of multifocal para-aortic and para-vesical paragangliomas

Front Endocrinol (Lausanne). 2022 Aug 8:13:946496. doi: 10.3389/fendo.2022.946496. eCollection 2022.

Authors

San-Chao Xiong¹, Xing-Peng Di², Meng-Ni Zhang³, Kan Wu², Xiang Li²

Affiliations

¹ Department of Urology, Chengdu Second People's Hospital, Chengdu, China.
² Department of Urology, Institute of Urology, West China Hospital, Sichuan University, Chengdu, China.
³ Department of Pathology, Institute of Pathology, West China Hospital, Sichuan University, Chengdu, China.

Abstract

Background: Paragangliomas (PGLs) are uncommon tumors of uncertain malignant potential. Multifocal paragangliomas are scarcely reported in the literature.

Case summary: A 25-year-old male patient was reported for the first time with multifocal para-aortic and para-vesical PGLs. The diagnosis was identified by blood catecholamine tests and enhanced CT scan and MIBG scintigraphy. A resection surgery was performed for treatment and the immunochemistry test of the tumors presented the features of PGL.

Conclusion: A case of multifocal para-aortic and para-vesical PGLs confirmed by the catecholamine test, enhanced CT, and MIBG scintigraphy is presented. The cooperation of experienced surgeons, anesthesiologists, and endocrinologists was critical in treatment.

Keywords: MIBG; case report; catecholamine; paraganglioma; surgery.

Publication types

Case Reports
Research Support, Non-U.S. Gov't

MeSH terms

3-Iodobenzylguanidine
Adrenal Gland Neoplasms*
Adult
Catecholamines
Humans
Male
Paraganglioma* / diagnostic imaging
Paraganglioma* / surgery
Pheochromocytoma*

Substances

Catecholamines
3-Iodobenzylguanidine