Cancer mortality among relatives of children with soft-tissue sarcoma: a national survey in Italy

Cancer Lett. 1987 Oct;37(1):17-24. doi: 10.1016/0304-3835(87)90141-8.

Abstract

Information was obtained on the living status or cause of death of 2223 close relatives of 195 children with soft-tissue sarcomas (STS) diagnosed under age 15. Three-hundred nine relatives had died, from all causes, before STS diagnosis in the index child. The expected figure estimated from age- and sex-specific mortality rates in Italy was 293.3. Cancer was reported as cause of death in 76 relatives (75.1 expected). Seven grandmothers, 2 aunts, 1 uncle and 0 mothers died from breast cancer vs. 4.6, 0.9, 0.0 and 0.2 expected. Three siblings died from cancer (0.2 expected, P less than 0.01), i.e. STS, ependymoma and non-Hodgkin lymphoma. These results confirm and expand previous observations that STS in children are associated with other cancers, particularly childhood and breast cancer, in members of the same family.

Publication types

  • Research Support, Non-U.S. Gov't

MeSH terms

  • Adolescent
  • Adult
  • Age Factors
  • Child
  • Child, Preschool
  • Female
  • Health Surveys
  • Humans
  • Infant
  • Italy
  • Male
  • Middle Aged
  • Pedigree
  • Retrospective Studies
  • Rhabdomyosarcoma / genetics
  • Sarcoma / genetics*
  • Sarcoma / mortality
  • Sex Factors
  • Soft Tissue Neoplasms / genetics*
  • Soft Tissue Neoplasms / mortality