Fontan completion of a 10-year-old Kawashima patient with extensive arteriovenous malformations: consideration for a lobectomy

Cardiol Young. 2023 Sep;33(9):1713-1714. doi: 10.1017/S1047951123000288. Epub 2023 Mar 10.

Abstract

A significant contributing factor to the progression of late cyanosis in individuals undergoing Kawashima operation is pulmonary arteriovenous malformations. Following the Fontan procedure, arteriovenous malformations may regress. However, in cases with extensive malformations causing severe cyanosis, lobectomy can also be a possible treatment approach. Thereby, we present our two-step treatment strategy in a late Fontan completion complicated by arteriovenous malformations in a Kawashima patient.

Keywords: Fontan; Kawashima; Lobectomy; arteriovenous malformation.

MeSH terms

  • Arteriovenous Fistula* / complications
  • Arteriovenous Fistula* / diagnosis
  • Arteriovenous Fistula* / surgery
  • Arteriovenous Malformations* / diagnosis
  • Arteriovenous Malformations* / surgery
  • Child
  • Cyanosis / complications
  • Fontan Procedure* / adverse effects
  • Humans
  • Pulmonary Artery / abnormalities
  • Pulmonary Artery / diagnostic imaging
  • Pulmonary Artery / surgery