Attack phenotypes and disease course in pediatric MOGAD

Ann Clin Transl Neurol. 2023 May;10(5):672-685. doi: 10.1002/acn3.51759. Epub 2023 Mar 31.

Abstract

Myelin oligodendrocyte glycoprotein antibody-associated disease (MOGAD) is an autoimmune demyelinating condition that affects children differently than adults. We performed a literature review to assess the presentation and clinical course of pediatric MOGAD. The most common initial phenotype is acute disseminated encephalomyelitis, especially among children younger than five years, followed by optic neuritis (ON) and/or transverse myelitis. Approximately one-quarter of children with MOGAD have at least one relapse that typically occurs within three years of disease onset and often includes ON, even if ON was not present at onset. Clinical risk factors for a relapsing course have not been elucidated.

Publication types

  • Review
  • Research Support, Non-U.S. Gov't

MeSH terms

  • Autoantibodies*
  • Disease Progression
  • Humans
  • Myelin-Oligodendrocyte Glycoprotein
  • Neoplasm Recurrence, Local
  • Optic Neuritis* / diagnosis
  • Phenotype

Substances

  • Autoantibodies
  • Myelin-Oligodendrocyte Glycoprotein

Grants and funding

This work was funded by UCB.