Hippocampal Reduction of α-Synuclein via RNA Interference Improves Neuropathology in Alzheimer's Disease Mice

J Alzheimers Dis. 2023;95(1):349-361. doi: 10.3233/JAD-230232.

Abstract

Background: Alzheimer's disease (AD) cases are often characterized by the pathological accumulation of α-synuclein (α-syn) in addition to amyloid-β (Aβ) and tau hallmarks. The role of α-syn has been extensively studied in synucleinopathy disorders, but less so in AD. Recent studies have shown that α-syn may also play a role in AD and its downregulation may be protective against the toxic effects of Aβ accumulation.

Objective: We hypothesized that selectively knocking down α-syn via RNA interference improves the neuropathological and biochemical findings in AD mice.

Methods: Here we used amyloid precursor protein transgenic (APP-Tg) mice to model AD and explore pathologic and behavioral phenotypes with knockdown of α-syn using RNA interference. We selectively reduced α-syn levels by stereotaxic bilateral injection of either LV-shRNA α-syn or LV-shRNA-luc (control) into the hippocampus of AD mice.

Results: We found that downregulation of α-syn results in significant reduction in the number of Aβ plaques. In addition, mice treated with LV-shRNA α-syn had amelioration of abnormal microglial activation (Iba1) and astrocytosis (GFAP) phenotypes in AD mice.

Conclusion: Our data suggests a novel link between Aβ and α-syn pathology as well as a new therapeutic angle for targeting AD.

Keywords: Alzheimer’s disease; alpha-synuclein; amyloid-β; biomarkers; lentivirus.

Publication types

  • Research Support, N.I.H., Extramural

MeSH terms

  • Alzheimer Disease* / pathology
  • Amyloid beta-Peptides / metabolism
  • Amyloid beta-Protein Precursor / genetics
  • Animals
  • Disease Models, Animal
  • Hippocampus / pathology
  • Mice
  • Mice, Transgenic
  • Plaque, Amyloid / pathology
  • RNA Interference
  • RNA, Small Interfering / genetics
  • RNA, Small Interfering / metabolism
  • alpha-Synuclein / genetics
  • alpha-Synuclein / metabolism
  • tau Proteins / metabolism

Substances

  • alpha-Synuclein
  • Amyloid beta-Protein Precursor
  • Amyloid beta-Peptides
  • RNA, Small Interfering
  • tau Proteins